BCKDHB antibody

Principal name

BCKDHB antibody

Alternative names for BCKDHB antibody

alpha-keto acid dehydrogenase, 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial Branched-chain alpha-keto acid dehydrogenase E1 component beta chain

SwissProt ID

P21839 (Bovin), P21953 (Human), P35738 (Rat), Q6P3A8 (Mouse)

Gene ID

594 (BCKDHB)

Available reactivities

Hu (Human), Ms (Mouse), Rt (Rat)

Available hosts

Rabbit

Available applications

Western blot / Immunoblot (WB), Immunocytochemistry/Immunofluorescence (ICC/IF), Paraffin Sections (P), Flow Cytometry (F), Enzyme Immunoassay (E)

Background of BCKDHB antibody

Branched-chain keto acid dehydrogenase is a multienzyme complex associated with the inner membrane of mitochondria, and functions in the catabolism of branched-chain amino acids. The complex consists of multiple copies of 3 components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). This gene encodes the E1 beta subunit, and mutations therein have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation, and feeding problems. Alternative splicing at this locus results in transcript variants with different 3' non-coding regions, but encoding the same isoform. [provided by RefSeq]. Transcript Variant: This variant (1) represents the longer transcript. Both variants 1 and 2 encode the same protein. Sequence Note: This RefSeq record was created from transcript and genomic sequence data to make the sequence consistent with the reference genome assembly. The extent of this transcript is supported by transcript alignments. Publication Note: This RefSeq record includes a subset of the publications that are available for this gene. Please see the Entrez Gene record to access additional publications.

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  2. Highly Validated (1)

7 Item(s)

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Primary Antibodies

Catalog No. Host Iso. Clone Pres. React. Applications  

BCKDHB (N-term) antibody

BCKDHB Antibody (N-term) (Cat. #TA324362) western blot analysis in Hela cell line lysates (35ug/lane).This demonstrates the BCKDHB antibody detected the BCKDHB protein (arrow). Rabbit Ig Aff - Purified Hu F, ICC/IF, P, WB
0.4 ml / €325.00
  OriGene Technologies, Inc.

BCKDHB antibody

Host: Rabbit; Target Name: BCKDHB; Sample Tissue: Thyroid tumor lysates; Antibody Dilution: 1.0 ug/ml Rabbit IgG Purified Hu WB
50 µg / €325.00
  OriGene Technologies, Inc.

BCKDHB antibody

Immunohistochemistry-Paraffin: BCKDHB Antibody [NBP1-86326] - Immunohistochemical staining of human stomach shows strong cytoplasmic positivity(granular pattern) in glandular cells. Rabbit IgG Aff - Purified Hu P, WB
0.1 ml / €500.00
  Novus Biologicals Inc.

Proteins & Growth Factors

Catalog No. Species Pres. Purity Source  

BCKDHB (transcript variant 1)

BCKDHB Human > 80 %
Preparation: Recombint protein was captured through anti-DDK affinity column followed by conventiol chromatography steps.
Purity Detail: > 80% as determined by SDS-PAGE and Coomassie blue staining.
HEK293 cells
20 µg / €680.00
  OriGene Technologies, Inc.

BCKDHB

BCKDHB Human 12.5% SDS-PAGE Stained with Coomassie Blue. in vitro transl.
2 µg / €300.00
  Abnova Taiwan Corp.

Lysates (Overexpressed)

Catalog No.    

BCKDHB overexpression lysate

BCKDHB overexpression lysate  
0.1 mg / €280.00
  OriGene Technologies, Inc.

BCKDHB overexpression lysate

BCKDHB overexpression lysate  
0.1 mg / €280.00
  OriGene Technologies, Inc.

7 Item(s)

per page
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