Cystinosin antibody

Principal name

Cystinosin antibody

Alternative names for Cystinosin antibody

CTNS

SwissProt ID

A7MB63 (Bovin), O60931 (Human), P57757 (Mouse)

Gene ID

1497 (CTNS)

Available reactivities

Hu (Human), Ms (Mouse), Rt (Rat), Bov (Bovine), Can (Canine), Eq (Equine), Por (Porcine), Rb (Rabbit)

Available hosts

Mouse, Rabbit

Available applications

Enzyme Immunoassay (E), Western blot / Immunoblot (WB), Paraffin Sections (P), ELISA (detection) (E(detection))

Background of Cystinosin antibody

Cystinosis is an autosomal recessive disorder resulting from defective lysosomal transport of cystine and present at birth as a failure to thrive, rickets and proximal renal tubular acidosis. The human CTNS gene on chromosome 17p13 encodes the protein Cystinosin, and mutations in CTNS are responsible for nephropathic cystinosis. The CTNS promoter contains an Sp1 binding element. Cystinosin is an integral membrane protein containing 7 transmembrane domains that functions as a H+-driven transporter responsible for cystine export from lysosomes. In humans, Cystinosin is expressed abundantly in pancreas, kidney (mature and fetal), and skeletal muscle. The mouse homolog to CTNS encodes a protein which is expressed in all tissues except skeletal muscle. In the cell, Cystinosin co-localizes with LAMP-2 to lysosomes. A C-terminal GYDQL sorting motif within Cystinosin is critical for lysosomal localization.

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Primary Antibodies

Catalog No. Host Iso. Clone Pres. React. Applications  

Cystinosin antibody

Cystinosin Rabbit IgG Purified Bov, Can, Eq, Hu, Ms, Por, Rb, Rt WB
50 µg / €325.00
  OriGene Technologies, Inc.

Cystinosin (268-285) antibody

Skeletal muscle: Formalin-Fixed Paraffin-Embedded (FFPE) Rabbit Purified Hu E, P
50 µg / €470.00
  Acris Antibodies GmbH

Cystinosin antibody

CTNS polyclonal antibody (A01), Lot # 060623JCS1 Western Blot analysis of CTNS expression in HeLa ( Cat # L013V1 ). Mouse Serum Hu E, WB
50 µl / €290.00
  Abnova Taiwan Corp.

Cystinosin antibody

Western Blot analysis of CTNS expression in transfected 293T cell line (H00001497-T01) by CTNS MaxPab polyclonal antibody.

Lane 1: CTNS transfected lysate(45.10 KDa).
Lane 2: Non-transfected lysate. Rabbit Purified Hu E(detection), WB
0.1 mg / €380.00
  Abnova Taiwan Corp.

Cystinosin antibody

CTNS monoclonal antibody (M09), clone 5G6 Western Blot analysis of CTNS expression in HepG2 ( Cat # L019V1 ). Mouse IgG2a 5G6 Purified Hu, Ms, Rt E, WB
0.1 mg / €370.00
  Abnova Taiwan Corp.

Cystinosin antibody

Cystinosin Rabbit Purified Hu E, P
50 µg / €480.00
  Novus Biologicals Inc.

Proteins & Growth Factors

Catalog No. Species Pres. Purity Source  

Cystinosin (transcript variant 2)

Cystinosin Human > 80 %
Preparation: Recombint protein was captured through anti-DDK affinity column followed by conventiol chromatography steps.
Purity Detail: > 80% as determined by SDS-PAGE and Coomassie blue staining.
HEK293 cells
20 µg / €680.00
  OriGene Technologies, Inc.

Cystinosin

Cystinosin Human
2 µg / €300.00
  Abnova Taiwan Corp.

Cystinosin

Cystinosin Human Purified 12.5% SDS-PAGE Stained with Coomassie Blue
10 µg / €380.00
  Abnova Taiwan Corp.

Cystinosin

Cystinosin Human Purified 12.5% SDS-PAGE Stained with Coomassie Blue
25 µg / €510.00
  Abnova Taiwan Corp.

Cystinosin

Cystinosin Human 12.5% SDS-PAGE Stained with Coomassie Blue. in vitro transl.
10 µg / €380.00
  Abnova Taiwan Corp.

Cystinosin

Cystinosin Human 12.5% SDS-PAGE Stained with Coomassie Blue. in vitro transl.
25 µg / €510.00
  Abnova Taiwan Corp.

Lysates

Catalog No.    

CTNS 293T Cell Transient Overexpression Lysate(Denatured)

CTNS 293T Cell Transient Overexpression Lysate(Denatured)  
0.1 ml / €270.00
  Abnova Taiwan Corp.

CTNS overexpression lysate

CTNS overexpression lysate  
0.1 mg / €280.00
  OriGene Technologies, Inc.

CTNS overexpression lysate

CTNS overexpression lysate  
0.1 mg / €280.00
  OriGene Technologies, Inc.

CTNS overexpression lysate

CTNS overexpression lysate  
0.1 mg / €280.00
  OriGene Technologies, Inc.

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