Fumarase antibody

Principal name

Fumarase antibody

Alternative names for Fumarase antibody

HLRCC, LRCC, MCL, MCUL1, mitochondrial Fumarate hydratase

SwissProt ID

P07954 (Human), P10173 (Pig), P14408 (Rat), P97807 (Mouse)

Gene ID

2271 (FH)

Available reactivities

Hu (Human), Por (Porcine), Bov (Bovine), Can (Canine), Chk (Chicken), Eq (Equine), Fi (Fish), Hst (Hamster), Insect, Mky (Monkey), Ms (Mouse), Op (Opossum), Prim (Primate), Rt (Rat), Sh (Sheep), Xen (Xenopus), Tr (Turkey), L (Lizard), Bear

Available hosts

Mouse, Goat, Rabbit

Available applications

Enzyme Immunoassay (E), Immunocytochemistry/Immunofluorescence (ICC/IF), Western blot / Immunoblot (WB), Paraffin Sections (P), Dot blot (Dot), Immunodiffusion (ID), Immunoprecipitation (IP), Radioimmunoassay (R), Flow Cytometry (F)

Background of Fumarase antibody

Defects in FH are the cause of fumarase deficiency (FHD) [MIM:606812]; also known as fumaricaciduria. FHD is characterized by progressive encephalopathy, developmental delay, hypotonia, cerebral atrophy and lactic and pyruvic acidemia.
Defects in FH are the cause of multiple cutaneous and uterine leiomyomata (MCUL1) [MIM:150800]. MCUL1 is an autosomal dominant condition in which affected individuals develop benign smooth muscle tumors (leiomyomata) of the skin. Affected females also usually develop leiomyomata of the uterus (fibroids).
Defects in FH are the cause of hereditary leiomyomatosis and renal cell cancer (HLRCC) [MIM:605839].

General readings

Lehtonen R., et al. (2003) J. Med. Genet. 40 (3): e19.
Toro JR., et al. (2003) Am. J. Hum. Genet. 73(1): 95-106.

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Primary Antibodies

Catalog No. Host Iso. Clone Pres. React. Applications  

Fumarase antibody

  Rabbit Polyclonal antibody to Fumarate hydratase (fumarate hydratase)  
Fumarate hydratase antibody [N2C2], Internal detects FH protein by Western blot analysis. A. 50 ug mouse liver lysate/extract. 10% SDS-PAGE. Fumarate hydratase antibody [N2C2], Internal (TA307962) dilution: 1:1000. Rabbit IgG Aff - Purified Hu, Ms, Rt ICC/IF, P, WB
0.1 ml / €325.00
  OriGene Technologies, Inc.

Fumarase antibody

  Rabbit polyclonal antibody to fumarate hydratase (fumarate hydratase)  
Fumarate hydratase antibody detects FH protein by Western blot analysis. A. 50 ug mouse liver lysate/extract. 7.5% SDS-PAGE. Fumarate hydratase antibody (TA307996) dilution: 1:1000. Rabbit IgG Aff - Purified Hu, Ms, Rt ICC/IF, P, WB
0.1 ml / €325.00
  OriGene Technologies, Inc.

Fumarase antibody

  FH (Fumarate Hydratase) mouse monoclonal antibody, clone OTI1F10 (formerly 1F10)  
Immunohistochemical staining of paraffin-embedded Human colon tissue within the normal limits using anti-FH mouse monoclonal antibody. (Heat-induced epitope retrieval by 10mM citric buffer, pH6.0, 100C for 10min, TA500675) Mouse IgG1 OTI1F10 Purified Can, Hu, Rt F, ICC/IF, P, WB
0.1 ml / €325.00
  OriGene Technologies, Inc.

TrueMAB

Fumarase antibody

  FH (Fumarate Hydratase) mouse monoclonal antibody, clone OTI2A2 (formerly 2A2)  
Immunofluorescent staining of HeLa cells using anti-FH mouse monoclonal antibody (TA500681). Mouse IgG1 OTI2A2 Purified Can, Hu ICC/IF, WB
0.1 ml / €325.00
  OriGene Technologies, Inc.

TrueMAB

Fumarase antibody

  FH mouse monoclonal antibody, clone OTI9G4 (formerly 9G4)  
Immunohistochemical staining of paraffin-embedded Human breast tissue within the normal limits using anti-FH mouse monoclonal antibody. (Heat-induced epitope retrieval by 10mM citric buffer, pH6.0, 100C for 10min, TA500682) Mouse IgG1 OTI9G4 Purified Can, Hu, Rt F, ICC/IF, P, WB
0.1 ml / €379.00
  OriGene Technologies, Inc.

TrueMAB

Fumarase antibody

  Rabbit Polyclonal Fumarase Antibody  
Immunohistochemical staining of human small intestine shows strong cytoplasmic positivity with a granular pattern in glandular cells.This validation was performed by Protein Atlas and the presentation of data is for informational purposes only. Rabbit IgG Purified Hu E, ICC/IF, P, WB
0.1 mg / €325.00
  OriGene Technologies, Inc.

Fumarase antibody

  Goat Polyclonal Antibody against Fumarase / FH  
TA302493 (0.01µg/ml) staining of Human Kidney lysate (35µg protein in RIPA buffer).  Primary incubation was 1 hour.  Detected by chemiluminescence. Goat Aff - Purified Can, Hu, Ms, Rt E, WB
0.1 mg / €325.00
  OriGene Technologies, Inc.

Fumarase antibody

  Rabbit anti-FH Polyclonal Antibody  
Western blot analysis of extracts of various cell lines, using FH antibody. Rabbit IgG Purified Hu, Ms, Rt
0.1 mg / €325.00
  OriGene Technologies, Inc.

Fumarase antibody

  Rabbit Polyclonal Anti-FH Antibody  
Gel: 8%SDS-PAGE, Lysate: 40 ug, Lane 1-4: Mouse liver tissue, Mouse brain tissue, Mouse heart tissue, RAW264.7 cells, Primary antibody: (FH Antibody) at dilution 1/850, Secondary antibody: Goat anti rabbit IgG at 1/8000 dilution, Exposure time: 20 seconds Rabbit IgG Purified Hu, Ms, Rt E, P, WB
0.1 ml / €325.00
  OriGene Technologies, Inc.

Fumarase antibody

The Cell lysates (40ug) were resolved by SDS-PAGE, transferred to PVDF membrane and probed with anti-human Fumarase antibody (1:1000). Proteins were visualized using a goat anti-mouse secondary antibody conjugated to HRP and an ECL detection system.

Lane 1. : HeLa cell lysate
Lane 2. : LNCap cell lysate
Lane 3. : A549 cell lysate
Lane 4. : HepG2 cell lysate
Lane 5. : 293T cell lysate
Lane 6. : K562 cell lysate
Lane 7. : Jurkat cell lysate Mouse IgG2a AT3F6 Purified Hu E, WB
0.1 ml / €310.00
  Acris Antibodies GmbH

Fumarase antibody

The Cell lysates (40ug) were resolved by SDS-PAGE, transferred to PVDF membrane and probed with anti-human Fumarase antibody (1:1000). Proteins were visualized using a goat anti-mouse secondary antibody conjugated to HRP and an ECL detection system.

Lane 1. : HeLa cell lysate
Lane 2. : LNCap cell lysate
Lane 3. : A549 cell lysate
Lane 4. : HepG2 cell lysate
Lane 5. : 293T cell lysate
Lane 6. : K562 cell lysate
Lane 7. : Jurkat cell lysate Mouse IgG2a AT3F6 Purified Hu E, WB
50 µl / €220.00
  Acris Antibodies GmbH

Fumarase antibody

Fumarase Rabbit IgG Azide Free Por Dot, E, ICC/IF, ID, IP, R, WB
10 mg / €240.00
  Acris Antibodies GmbH

Fumarase antibody

Fumarase Rabbit IgG Biotin Por Dot, E, ICC/IF, ID, IP, R, WB
1 ml / €350.00
  Acris Antibodies GmbH

Fumarase antibody

Fumarase Rabbit IgG Aff - Purified Por Dot, E, ICC/IF, ID, IP, R, WB
1 mg / €440.00
  Acris Antibodies GmbH

Fumarase (176-189) antibody

Human Heart: Formalin-Fixed, Paraffin-Embedded (FFPE) Goat Aff - Purified Bear, Bov, Can, Chk, Elephant, Eq, Fi, Hst, Hu, Insect, L, Mky, Ms, Op, Platypus, Por, Prim, Rt, Sh, Tr, Xen E, P, WB
50 µg / €470.00
  Acris Antibodies GmbH

CRISPR

Catalog No. Species Donor Vector  

FH - human gene knockout kit via CRISPR

FH - human gene knockout kit via CRISPR Human GFP-Puro
1 kit / €1,200.00
  OriGene Technologies, Inc.

FH - human gene knockout kit via CRISPR

FH - human gene knockout kit via CRISPR Human mBFP-Neo
1 kit / €1,290.00
  OriGene Technologies, Inc.

FH - human gene knockout kit via CRISPR

FH - human gene knockout kit via CRISPR Human Luciferase-Puro
1 kit / €1,290.00
  OriGene Technologies, Inc.

FH - human gene knockout kit via CRISPR

FH - human gene knockout kit via CRISPR Human RFP-BSD
1 kit / €1,290.00
  OriGene Technologies, Inc.

Proteins & Growth Factors

Catalog No. Species Pres. Purity Source  

Fumarase

  Recombinant protein of human fumarate hydratase (FH), nuclear gene encoding mitochondrial protein  
Fumarase Human > 80 %
Preparation: Recombint protein was captured through anti-DDK affinity column followed by conventiol chromatography steps.
Purity Detail: > 80% as determined by SDS-PAGE and Coomassie blue staining.
HEK293 cells

Regular Price: 20 µg / €680.00

Special Price: 20 µg / €398.00

  OriGene Technologies, Inc.

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