GBE1 antibody

Principal name

GBE1 antibody

Alternative names for GBE1 antibody

Glycogen-branching enzyme, Brancher enzyme, 1,4-alpha-glucan-branching enzyme

SwissProt ID

Q04446 (Human), Q9D6Y9 (Mouse)

Gene ID

2632 (GBE1)

Available reactivities

Hu (Human), Ms (Mouse), Rt (Rat)

Available hosts

Mouse, Rabbit

Available applications

Enzyme Immunoassay (E), Western blot / Immunoblot (WB), ELISA (detection) (E(detection)), Immunocytochemistry/Immunofluorescence (ICC/IF), Paraffin Sections (P), Immunoprecipitation (IP), Flow Cytometry (F), Frozen Sections (C)

Background of GBE1 antibody

GBE1 is a 702 amino acid protein that is expressed at high levels in muscle and liver and is involved in glycogen biosynthesis. Existing as a monomer, GBE1 catalyzes the transfer of alpha-1,4-linked glucosyl units from the outer end of a glycogen chain to an alpha-1,6 position on a neighboring glycogen chain and, via this catalytic activity, plays an essential role in glycogen accumulation. Defects in the gene encoding GBE1 are the cause of glycogen storage disease type 4 (GSD4) and adult polyglucosan body disease (APBD), the first of which is a metabolic disorder that is associated with the accumulation of polysaccharides and is characterized by liver disease during childhood. Unlike GSD4, APBD is a late-onset disorder that affects the central and peripheral nervous systems and is characterized by cognitive impairment, pyramidal tetraparesis and peripheral neuropathy.

General readings

Konstantinidou, A.E., et al. Placenta 29(4):378-381(2008)
Massa, R., et al. Muscle Nerve 37(4):530-536(2008)
Bruno, C., et al. Acta Myol 26(1):75-78(2007)

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Primary Antibodies

Catalog No. Host Iso. Clone Pres. React. Applications  

GBE1 antibody

Immunohistochemical staining of paraffin-embedded Human pancreas tissue within the normal limits using anti-GBE1 mouse monoclonal antibody. (Heat-induced epitope retrieval by 10mM citric buffer, pH6.0, 100C for 10min, TA500801) Mouse IgG2a OTI3B4 Purified Hu IP, P, WB
0.1 ml / €325.00
  OriGene Technologies, Inc.

TrueMAB

GBE1 antibody

Anti-GBE1 mouse monoclonal antibody (TA500807) immunofluorescent staining of COS7 cells transiently transfected by pCMV6-ENTRY GBE1(RC204152). Mouse IgG2a OTI4D9 Purified Hu F, ICC/IF, IP, WB
0.1 ml / €325.00
  OriGene Technologies, Inc.

TrueMAB

GBE1 antibody

Immunohistochemical staining of paraffin-embedded Human endometrium tissue within the normal limits using anti-GBE1 mouse monoclonal antibody. (Heat-induced epitope retrieval by 10mM citric buffer, pH6.0, 100C for 10min, TA500829) Mouse IgG1 OTI1D11 Purified Hu F, ICC/IF, IP, P, WB
0.1 ml / €379.00
  OriGene Technologies, Inc.

TrueMAB

GBE1 antibody

Immunohistochemical staining of paraffin-embedded Carcinoma of Human liver tissue using anti-GBE1 mouse monoclonal antibody. (Heat-induced epitope retrieval by 10mM citric buffer, pH6.0, 100C for 10min, TA500779) Mouse IgG1 OTI4E6 Purified Hu IP, P, WB
0.1 ml / €325.00
  OriGene Technologies, Inc.

TrueMAB

GBE1 antibody

Immunohistochemical staining of paraffin-embedded Human pancreas tissue within the normal limits using anti-GBE1 mouse monoclonal antibody. (Heat-induced epitope retrieval by 10mM citric buffer, pH6.0, 100C for 10min, TA500802) Mouse IgG1 OTI5B7 Purified Hu F, IP, P, WB
0.1 ml / €325.00
  OriGene Technologies, Inc.

TrueMAB

GBE1 antibody

Immunohistochemical staining of paraffin-embedded Human Ovary tissue within the normal limits using anti-GBE1 mouse monoclonal antibody. (Heat-induced epitope retrieval by 10mM citric buffer, pH6.0, 100C for 10min, TA500803) Mouse IgG1 OTI3C8 Purified Hu F, IP, P, WB
0.1 ml / €325.00
  OriGene Technologies, Inc.

TrueMAB

GBE1 antibody

Immunohistochemical staining of paraffin-embedded Human Kidney tissue within the normal limits using anti-GBE1 mouse monoclonal antibody. (Heat-induced epitope retrieval by 10mM citric buffer, pH6.0, 100C for 10min, TA500846) Mouse IgG1 OTI4A1 Purified Hu F, ICC/IF, IP, P, WB
0.1 ml / €325.00
  OriGene Technologies, Inc.

TrueMAB

GBE1 (Center) antibody

Confocal immunofluorescent analysis of GBE1 Antibody (Center) Cat.-No AP51790PU-N with HepG2 cell followed by Alexa Fluor? 488-conjugated goat anti-rabbit lgG (green). Actin filaments have been labeled with Alexa Fluor 555 phalloidin (red). DAPI was used to stain the cell nuclear (blue). Rabbit Ig Aff - Purified Hu, Ms ICC/IF, WB
0.4 ml / €370.00
  Acris Antibodies GmbH

GBE1 antibody

GBE1 Mouse Serum Hu E, WB
50 µl / €290.00
  Abnova Taiwan Corp.

GBE1 antibody

GBE1 MaxPab polyclonal antibody. Western Blot analysis of GBE1 expression in human liver. Mouse Purified Hu E(detection), WB
50 µg / €370.00
  Abnova Taiwan Corp.

GBE1 antibody

GBE1 Rabbit Serum Hu IP, WB
0.1 ml / €380.00
  Abnova Taiwan Corp.

GBE1 antibody

Western Blot analysis of GBE1 expression in transfected 293T cell line (H00002632-T01) by GBE1 MaxPab polyclonal antibody.

Lane 1: GBE1 transfected lysate(80.40 KDa).
Lane 2: Non-transfected lysate. Rabbit Purified Hu E(detection), WB
0.1 mg / €380.00
  Abnova Taiwan Corp.

GBE1 antibody

Immunohistochemistry-Paraffin: GBE1 Antibody [NBP1-85875] - Immunohistochemical staining of human kidney shows strong cytoplasmic positivity in cells in tubule. Rabbit IgG Aff - Purified Hu P, WB
0.1 ml / €500.00
  Novus Biologicals Inc.

Proteins & Growth Factors

Catalog No. Species Pres. Purity Source  

GBE1

GBE1 Human > 80 %
Preparation: Recombint protein was captured through anti-DDK affinity column followed by conventiol chromatography steps.
Purity Detail: > 80% as determined by SDS-PAGE and Coomassie blue staining.
HEK293 cells
20 µg / €680.00
  OriGene Technologies, Inc.

GBE1

GBE1 Human Purified 12.5% SDS-PAGE Stained with Coomassie Blue.
10 µg / €380.00
  Abnova Taiwan Corp.

GBE1

GBE1 Human Purified 12.5% SDS-PAGE Stained with Coomassie Blue.
25 µg / €510.00
  Abnova Taiwan Corp.

GBE1

GBE1 Human 12.5% SDS-PAGE Stained with Coomassie Blue. in vitro transl.
10 µg / €380.00
  Abnova Taiwan Corp.

GBE1

GBE1 Human 12.5% SDS-PAGE Stained with Coomassie Blue. in vitro transl.
25 µg / €510.00
  Abnova Taiwan Corp.

Antibody Pairs

Catalog No.    

GBE1 (Human) IP-WB Antibody Pair

GBE1 (Human) IP-WB Antibody Pair  
1 set / €710.00
  Abnova Taiwan Corp.

Lysates

Catalog No.    

GBE1 293T Cell Transient Overexpression Lysate(Denatured)

GBE1 293T Cell Transient Overexpression Lysate(Denatured)  
0.1 ml / €270.00
  Abnova Taiwan Corp.

20 Item(s)

per page
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